Cor Vasa 2015, 57(3):e228-e233 | DOI: 10.1016/j.crvasa.2014.11.001

Persistent left superior vena cava, absent right superior vena cava and coronary-bronchial fistula: The good, the bad and the ugly (case report and review of literature)

Jiří Plášek^a,b,*, Tomáš Veiser^a, David Šipula^a, Miroslav Homza^a,b

^a Kardiovaskulární oddělení, Fakultní nemocnice Ostrava, Ostrava, Česká republika

^b Lékařská fakulta Ostravské univerzity, Ostrava, Česká republika

A 62-year-old Caucasian male presented with syncope during casual daily activity without preceding prodromes. During ECG Holter monitoring, we observed numerous asystolic pauses lasting >4 s due to sino-atrial blockade and sinus bradycardia. During pacemaker implantation, persistent left superior vena cava with agenesis of the right superior vena cava was diagnosed. Unproblematic placement of atrial lead was followed by challenging placement of the right ventricular lead. Anterior position with a sharp angulation to the right ventricular wall was achieved with excellent stimulation parameters. Transesophageal echocardiography confirmed the diagnosis of persistent left superior vena cava with agenesis of right superior vena cava. Moreover, selective coronary angiography showed connection between right coronary artery branch and bronchial vessel. To the best of our knowledge, we are the first to describe a combination of persistent left superior vena cava with absent right superior vena cava, coronary-bronchial fistula and conduction abnormality with the necessity of device implantation.

Keywords: Coronary-bronchial fistula; Isolated, persistent left superior vena cava; Pacemaker implantation

Received: August 23, 2014; Revised: October 24, 2014; Accepted: November 5, 2014; Published: June 1, 2015  Show citation