Cor Vasa 2011, 53(8-9):493-495 | DOI: 10.33678/cor.2011.121
Cardiogenic shock as a cause of death in a patient with Churg-Strauss syndrome
- 1 Interní oddělení - kardiovaskulární
- 2 Oddělení patologie, Městská nemocnice Ostrava, Ostrava, Česká republika
Churg-Strauss syndrome, also known as allergic granulomatosis, is a rare systemic disorder characterized by the following triad: bronchial asthma, hypereosinophilia with extravascular eosinophilic granulomas and vasculitis of small- and middle-sized vessels, leading to their necrosis. The vasculitis predominantly affects pulmonary, skin and peripheral nerve vessels but also heart, gastrointestinal tract, kidney or central nervous system. Corticosteroids are the cornerstone of therapy. If untreated, the condition is fatal. Early institution of therapy improves the prognosis considerably.
Keywords: Churg-Strauss syndrome; Hypereosinophilia; Vasculitis; Cardiogenic shock
Published: August 1, 2011 Show citation
References
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