Cor Vasa 2025, 67(Suppl.3):68-70 | DOI: 10.33678/cor.2025.023

Surgical correction of partial anomalous pulmonary venous return in a patient with persistent left superior vena cava: cannulation techniques and challenges

Andrej Domonkosa, Panagiotis Artemioua, Štefan Durdíkb, Ivo Gašparoviča, Michal Hulmana
a Department of Cardiac Surgery, Faculty of Medicine of the Comenius University, National Institute for Cardiovascular Diseases, Bratislava, Slovakia
b Department of Surgical Oncology, Faculty of Medicine of the Comenius University, St. Elizabeth Oncology Institute, Bratislava, Slovakia

Partial anomalous pulmonary venous return (PAPVR) associated with a sinus venosus atrial septal defect (SVASD) and a persistent left superior vena cava (PLSVC) presents significant surgical challenges. These anomalies require careful planning of cardiopulmonary bypass (CPB) and venous cannulation strategies. A 38-year-old woman presented with a history of supraventricular tachycardia (SVT) and a hemodynamically significant left-to-right shunt (Qp : Qs = 1.87) due to SVASD and PAPVR. Preoperative imaging revealed drainage of the right upper pulmonary vein into the PLSVC. The patient underwent successful surgical cor- rection using the double-patch technique with cardiopulmonary bypass support via a complex cannulation strategy involving both superior venae cavae. Postoperatively, the patient recovered well, with no evidence of residual shunt or significant valvular dysfunction. The case highlights the surgical approach to a rare combination of anomalies and discusses alternative cannulation strategies for CPB in patients with PLSVC. Kľúčové slova: Chirurgická korekcia Parciálny anomálny návrat pľúcnych žíl Perzistujúca ľavá horná dutá žila Sínusový venózny defekt predsieňového septa Technika kanulácie Vrodená srdcová chyba

Keywords: Cannulation technique, Congenital heart disease, Partial anomalous pulmonary venous return, Persistent left superior vena cava, Sinus venosus atrial septal defect, Surgical correction,

Received: January 21, 2025; Revised: February 4, 2025; Accepted: February 7, 2025; Prepublished online: July 24, 2025; Published: September 1, 2025  Show citation

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Domonkos A, Artemiou P, Durdík Š, Gašparovič I, Hulman M. Surgical correction of partial anomalous pulmonary venous return in a patient with persistent left superior vena cava: cannulation techniques and challenges. Cor Vasa. 2025;67(Suppl.3):68-70. doi: 10.33678/cor.2025.023.
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