Cor Vasa 2013, 55(3):e236-e241 | DOI: 10.1016/j.crvasa.2012.11.001

Isolated non-compaction cardiomyopathy: A review

Renata Virtováa,*, Miloą Kubáneka, Marek ©ramkoa, Luděk Voskaa,b, Dana Kautznerováa,c, Josef Kautznera
a Klinika kardiologie, Institut klinické a experimentální medicíny, Praha, Česká republika
b Oddělení klinické a transplantační patologie, Institut klinické a experimentální medicíny, Praha, Česká republika
c Základna radiodiagnostiky, Institut klinické a experimentální medicíny, Praha, Česká republika

Non-kompaktní kardiomyopatie (LVNC) je vzácně se vyskytující onemocnění, které patří podle klasifikace Evropské kardiologické společnosti do kategorie neklasifikovaných kongenitálních kardiomyopatií. Pro LVNC je typické ztluątění stěny apikální části levé komory, podmíněné zvýąenou trabekularizací a hlubokými intertrabekulárními recesy komunikujícími s dutinou levé komory. Za příčinu tohoto stavu se povaľuje chybná embryogeneze endokardu a myokardu. Mezi klinické projevy LVNC patří srdeční selhání, tromboembolické příhody, arytmie a náhlá srdeční smrt. Průběh onemocnění je velmi variabilní, s obtíľně predikovatelným vývojem. Cílem této práce bylo poskytnout aktuální přehled informací o izolované LVNC.

Keywords: Echokardiografie; Genetika; Magnetická rezonance; Non-kompaktní kardiomyopatie; Výpočetní tomografie

Received: October 16, 2012; Accepted: November 1, 2012; Published: June 1, 2013  Show citation

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Virtová R, Kubánek M, ©ramko M, Voska L, Kautznerová D, Kautzner J. Isolated non-compaction cardiomyopathy: A review. Cor Vasa. 2013;55(3):e236-241. doi: 10.1016/j.crvasa.2012.11.001.
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