Cor Vasa 2010, 52(7-8):405-408 | DOI: 10.33678/cor.2010.110

Arrhythmogenic right ventricular cardiomyopathy

Jan Krejčí

I. interní kardioangiologická klinika, Fakultní nemocnice u sv. Anny a Lékařská fakulta Masarykovy univerzity, Brno, Česká republika

Arrhythmogenic right ventricular cardiomyopathy is a genetically-linked condition characterized by loss of the myocardium, particularly that of the right ventricle, to be replaced by adipose and fibrous tissue. The clinical picture is dominated by arrhythmias, with most patients dying suddenly. The diagnosis is based on search for the presence of major and minor criteria. Principal methods of examination include electrocardiography, Holter ECG monitoring, echocardiography, magnetic resonance imaging and, possibly, other methods. The key therapeutic consideration is prevention of sudden death, that is, management of arrhythmias and, most importantly, cardioverter-defibrillator implantation.

Keywords: Arrhythmogenic right ventricular cardiomyopathy; Clinical picture; Diagnosis; Treatment

Published: July 1, 2010  Show citation